Eisenmengers Syndrome with Scoliosis: Case Report

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Eisenmengers Syndrome with Scoliosis Case Report
M. Bulent Balioglu, Ali Oner, M. A Kaygusuz,
Osman Cimen, Serhan Ornek Ministry of Health
Metin Sabanci Baltalimani Bone Disease Hospital,
Istanbul, TURKEY
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Summary

• Case notes of a 12 year old patient diagnosed
  with Eisenmengers syndrome (ES) and scoliosis.

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Introduction

• ES is a complication of uncorrected congenital
  heart anomalies that produces left-to-right
  shunting.
• Increased pulmonary resistance often develops
  over time, reversing left-to-right shunting to
  right-to-left shunting.
• Scoliosis is present in about 1/3 of patients.

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Methods

• Our patient was 12 years old (female).
• Diagnosis of ES was made using standard cardiac
  techniques while spinal x-rays and spinal column
  MRIs were used to define the scoliosis.

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EO, 17.02.2009
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EO, Eisenmenger Syndrome with Scoliosis
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Results

• Untreated congenital heart anomalies that result
  in ES include ventricular septal defect,
  atrioventricular canal defect, atrial septal
  defect, persistent truncus arteriosus and
  transposition of the main arteries.
• Cardiac catheterization was peformed on the
  patient with adverse results.
• Surgery, either cardiac or spinal, is not
  advised.

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Conclusion

• Occasionally, very rare cardiac syndromes are
  encountered.
• Patients with severe thoracolumbaer scoliosis due
  to ES, can not be operated.
• Thus scoliosis is treated using a correction
  brace and close patient observation.